Idiopathic Pulmonary Fibrosis (IPF): An Overview
نویسندگان
چکیده
منابع مشابه
Current Concept for the Pathogenesis of Idiopathic Pulmonary Fibrosis (IPF)
Fibrosis in interstitial lung disease is caused by the accumulation of extracellular matrix proteins within the interstitium and alveolar space of the lung. The majority of severe cases comprise a classification known as idiopathic pulmonary fibrosis (IPF) for which the origin is unknown [1]. IPF is the most severe chronic form of pulmonary fibrosis and results in gradual exchange of normal lun...
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A 76-year-old Japanese man was diagnosed with idiopathic pulmonary fibrosis (IPF) based on high-resolution computed tomography (CT) (Picture A) three years prior. Nintedanib (300 mg/day) treatment was initiated to treat the IPF. Eighty-four days later, he visited our hospital with stomachache, chronic diarrhea and gross hematochezia. Abdominal contrast-enhanced CT showed bowel wall thickening (...
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Idiopathic pulmonary fibrosis (IPF) is a chronic lung condition of uncertain aetiology that should be considered in the differential diagnosis of patients who experience breathlessness, cough and reduced exercise tolerance. IPF is characterized histologically by the presence of usual interstitial pneumonia, and often has typical radiological appearances. Long-term successful management options ...
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Khalilzadeh S1, Baghaei N2, Bolorsaz MR1, Masjedi MR3 1. Associate professor, Department of pediatrics, Education, research and treatment center of tuberculosis and long diseases, Shahid Beheshti University of medical sciences 2. Assistant professor, Department of pediatrics, Education, research and treatment center of tuberculosis and long diseases, Shahid Beheshti University of medical s...
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A 25 year old male and his 46 year old aunt presented with shortness of breath and a dramatic response to steroids. The other two patients are sisters with more advanced disease. One of these responded partially to steroids, while the other died within 4 months of treatment. The genetic basis and pathogenesis are discussed.
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ژورنال
عنوان ژورنال: Journal of Clinical Medicine
سال: 2018
ISSN: 2077-0383
DOI: 10.3390/jcm7080201